Congenital Convex Pes Valgus
Michael D. Kotzen, D.P.M.
Overview
‱ Rare and disabling condition
‱ Presents with rigid rocker-bottom flatfoot
‱ Differentiated from other valgus conditions by it’s rigidity
‱ Talonavicular joint dislocated on X-ray
‱ Navicular dorsally dislocated
‱ Talus is locked in plantarflexion
‱ Important to recognize condition as treatment is different
from other flatfoot conditions
Incidence
‱ Less than 1% of live births
‱ Osmond and Clark study states .76% incidence in 1,319
infants
‱ Buchanan and Greer .64% incidence in a study containing
22,000 children
‱ Equal distribution between genders
‱ Usually bilateral but if unilateral right foot is the most
common
Etiology (theories)
‱ Exogenous forces create intrauterine pressure which forces
foot into valgus
‱ Endogenous forces such as decreased amniotic fluid
‱ Increased pressure from the tibia on the foot
‱ Arrest in development of talus in 2nd
intrauterine months
‱ Excessive action of peroneals in 4th
stage intrauterine life
‱ Absence of plantar intrinsic muscles
‱ Neuromuscular imbalance between Tibialis Posterior and
peroneals
Etiology (neuromuscular)
‱ Contracture of ankle dorsiflexors, Peroneal muscles, and
Triceps Surae
‱ Shortened dorsiflexors and Peroneals pull forefoot into
plantarflexion and valgus
‱ Triceps Surae holds Calcaneus in equinus
‱ Talus bound to Calcaneus by interosseous ligament so
Talus follows Calcaneus into plantarflexion
‱ Ligamentous attachments prevent Talus from everting
‱ Talus protrudes medially and plantarly
‱ Possible hereditary trisomy 13,15, and 18
Associated conditions
‱ Congenital dislocated hip
‱ Clubfoot
‱ Fusion of vertebrae
‱ Absence of patella
‱ Joint ankylosis
‱ Kyphosis
‱ Myelomengocele
‱ Ischiocalcaneus
‱ Whistling face syndrome
‱ Spina bifida
‱ Hernia
‱ Hypospadias
‱ Microcephalia
‱ Arthrogryphosis
‱ Cerebral palsy
‱ Endocrine disturbances
‱ Down’s syndrome
‱ Retardation of intellect
Clinical presentation
‱ Plantar aspect of foot is convex with severe rocker-bottom
appearance
‱ Talar head is palpable at the plantar medial aspect of the
foot
‱ Forefoot is abducted, dorsiflexed and everted
‱ Anterior and lateral muscles become tight and resist
plantarflexion and inversion
‱ Rearfoot is in equinus
‱ Rigidity is seen after 2 months of age
‱ Gait is akward and difficult, but delay in ambulation is not
noted because pain is not initially present
Radiographic evaluation
‱ Not all bones are visible in the newborn but x-rays still
show characteristic findings
‱ On AP you will see abduction of the forefoot and
increased Talo-Calcaneal angle
‱ On LAT you will see Talus vertical and parallel with the
Tibia, Calcaneus in equinus
‱ Foot is dorsiflexed and laterally deviated
‱ Talar bisection is inferior to first metatarsal bisection
‱ Navicular is dislocated in dorsal aspect of the Talus
Radiographic evaluation
Bone and joint changes
‱ Navicular does not articulate with the Talus but lies on the
dorsal aspect of the Talar head and neck
‱ Talar head is flattened superiorly and directed plantar medially
‱ Calcaneus is convex on the plantar surface and is locked in
rigid equinus
‱ Anterior facet of the Calcaneus is absent and the
Sustentaculum Tali is abnormal
‱ Lateral column is subluxed dorsolaterally at the
Calcaneocuboid joint
‱ Cuboid and Navicular articulation with metatarsals and
cuneiforms are normal
Tendon and muscle changes
‱ All anterior muscle group tendons are contracted across the
ankle joint
‱ Only the proximal section of the extensor retinaculum is
present
‱ Extensors are displaced laterally
‱ Tibialis posterior tendon is attenuated as it passes inferior
to the navicular
‱ Peroneal tendons are subluxed anterior to the malleoli
‱ Peroneal and Tibialis posterior tendons can act as
dorsiflexors
Ligamentous changes
‱ Tibionavicular band of the deltoid ligament is contracted
‱ Bifurcate, interosseous Talocalcaneal and Calcaneal
fibular ligaments are shortened
‱ Distal band of the extensor retinaculum absent and the
proximal part is thickened
‱ Ligaments along the medial plantar arch and long plantar
ligament are attenuated
‱ Posterior ankle and subtalar joint capsules are contracted
‱ Plantar medial capsule of Talonavicular joint is elongated
Vascular and nerve changes
‱ To date there are no physical complaints of vascular and
nerve abnormalities
‱ Some abnormal histological exams have been reported
‱ Congenital Convex Pes Valgus can be associated with
chronic proliferation endarteritis and neurofibromatosis
Differential diagnosis
‱ Talipes Calcaneal Valgus - presents as flexible deformity
‱ Flexible vertical Talus
‱ Spastic flatfoot secondary to CP, and Myelmenigocele-
can be reduced by using a nerve block to alleviate
spasticity
‱ Flatfoot secondary to coalition
Conservative treatment
‱ Object is to restore the anatomic relationship of Calcaneus
and Navicular to the Talus
‱ Conservative treatment alone is considered inadequate and
surgery is the mainstay of treatment
‱ Casting alone gets poor results, but can be beneficial in
stretching and manipulating anterior capsule and
contracted muscles pre-operatively
Surgical treatment
‱ Intervention is desired before 1 year of age
‱ Dodge proposed one stage open reduction and soft tissue release
at ages less than 3 years old
‱ Grice arthrodesis is suggested for children ages 3 or greater
‱ Clark place bone block at the STJ at ages up to 3 years old, if
greater than 3 years old perform STJ arthrodesis
‱ Griffen if surgery is delayed until 10-12 years old then perform
triple arthrodesis
‱ Tachdijian ORIF if less than 4 years old and have failed casting
and manipulation. If 4-6 years old, ORIF with TAL, posterior
ankle and STJ capsule release, with STJ arthrodesis
Tendon procedures
‱ Transfer Tibialis anterior tendon to Talar neck. Peroneus
Brevis tendon is anastomosed with Tibialis posterior
tendon and attached at the medial Navicular
‱ Duckworth and Smith Tibialis anterior tendon is
transferred to the neck of the Talus
‱ Goldner comprehensive release 4 incision approach for
release of all contracted joints and capsules, Tibialis
anterior and posterior tendons are transferred to the neck
of the Talus, Peroneus Brevis tendon is run through the
neck of the Talus, Talonavicular joint and STJ are released
Osseous procedures
‱ Talectomy (fallen out of favor)
‱ Removal of wedge from the Navicular under the Talar
head to maintain elevation of the medial column
‱ Navicularectomy with release remains a very effective
procedure
‱ Grice arthrodesis if less than 3 years of age
‱ Triple arthrodesis if 10-12 years of age
McGlamry preference
‱ Start manipulation and casting ASAP, twice a week for 6-8
weeks
‱ At 6-8 weeks attempt to relocate Talocalcanealnavicular
joint and pin if successful
‱ If not reducible by 4-6 months correct deformity by ORIF
‱ Medial incision is made from 1st
metatarsal/cuneiform
joint to distal aspect of the medial malleolus and
proximally to overlie Achilles tendon
‱ Lengthen the Achilles tendon
McGlamry preference
‱ Lengthen: Tibialis anterior, and Peroneals
‱ Release: Talonavicular ligament, Tibionavicular ligament,
Bifurcate ligament, Calcanealcuboid joint, Calcaneal
Fibular liagament, Interosseous Talocalcaneal ligament
‱ Foot is distracted and manipulated and k-wire is placed
from posterior Talar body through the Navicular and
Cuneiform into IM space
‱ Reefing of the Spring ligament and placement of a 2nd
k-
wire from the plantar foot through the Calcaneus and into
the Talus
McGlamry preference
‱ Close incision sites according to surgeon’s preference
‱ AK cast for 3-4 months
‱ Remove k-wire at 6 weeks
‱ Night time splint for 1 to 2 years
‱ Physical therapy
‱ Excise Navicular if the child is between the ages of 3-6 or
the deformity remains
‱ Triple arthrodesis if the child is 10-12 years of age
Post-op complications
‱ AVN of the Navicular or Talus
‱ Inadequate dorsiflexion
‱ Over correction of heel into Varus
‱ Development of bunion deformity
‱ Incomplete reduction
‱ Re-occurrence
‱ Continued Equinus
‱ Curly toes
‱ Stiffness
Thank you!

chapter 30 CCPV.ppt pes cavus, pes cavus

  • 1.
    Congenital Convex PesValgus Michael D. Kotzen, D.P.M.
  • 2.
    Overview ‱ Rare anddisabling condition ‱ Presents with rigid rocker-bottom flatfoot ‱ Differentiated from other valgus conditions by it’s rigidity ‱ Talonavicular joint dislocated on X-ray ‱ Navicular dorsally dislocated ‱ Talus is locked in plantarflexion ‱ Important to recognize condition as treatment is different from other flatfoot conditions
  • 3.
    Incidence ‱ Less than1% of live births ‱ Osmond and Clark study states .76% incidence in 1,319 infants ‱ Buchanan and Greer .64% incidence in a study containing 22,000 children ‱ Equal distribution between genders ‱ Usually bilateral but if unilateral right foot is the most common
  • 4.
    Etiology (theories) ‱ Exogenousforces create intrauterine pressure which forces foot into valgus ‱ Endogenous forces such as decreased amniotic fluid ‱ Increased pressure from the tibia on the foot ‱ Arrest in development of talus in 2nd intrauterine months ‱ Excessive action of peroneals in 4th stage intrauterine life ‱ Absence of plantar intrinsic muscles ‱ Neuromuscular imbalance between Tibialis Posterior and peroneals
  • 5.
    Etiology (neuromuscular) ‱ Contractureof ankle dorsiflexors, Peroneal muscles, and Triceps Surae ‱ Shortened dorsiflexors and Peroneals pull forefoot into plantarflexion and valgus ‱ Triceps Surae holds Calcaneus in equinus ‱ Talus bound to Calcaneus by interosseous ligament so Talus follows Calcaneus into plantarflexion ‱ Ligamentous attachments prevent Talus from everting ‱ Talus protrudes medially and plantarly ‱ Possible hereditary trisomy 13,15, and 18
  • 6.
    Associated conditions ‱ Congenitaldislocated hip ‱ Clubfoot ‱ Fusion of vertebrae ‱ Absence of patella ‱ Joint ankylosis ‱ Kyphosis ‱ Myelomengocele ‱ Ischiocalcaneus ‱ Whistling face syndrome ‱ Spina bifida ‱ Hernia ‱ Hypospadias ‱ Microcephalia ‱ Arthrogryphosis ‱ Cerebral palsy ‱ Endocrine disturbances ‱ Down’s syndrome ‱ Retardation of intellect
  • 7.
    Clinical presentation ‱ Plantaraspect of foot is convex with severe rocker-bottom appearance ‱ Talar head is palpable at the plantar medial aspect of the foot ‱ Forefoot is abducted, dorsiflexed and everted ‱ Anterior and lateral muscles become tight and resist plantarflexion and inversion ‱ Rearfoot is in equinus ‱ Rigidity is seen after 2 months of age ‱ Gait is akward and difficult, but delay in ambulation is not noted because pain is not initially present
  • 9.
    Radiographic evaluation ‱ Notall bones are visible in the newborn but x-rays still show characteristic findings ‱ On AP you will see abduction of the forefoot and increased Talo-Calcaneal angle ‱ On LAT you will see Talus vertical and parallel with the Tibia, Calcaneus in equinus ‱ Foot is dorsiflexed and laterally deviated ‱ Talar bisection is inferior to first metatarsal bisection ‱ Navicular is dislocated in dorsal aspect of the Talus
  • 10.
  • 11.
    Bone and jointchanges ‱ Navicular does not articulate with the Talus but lies on the dorsal aspect of the Talar head and neck ‱ Talar head is flattened superiorly and directed plantar medially ‱ Calcaneus is convex on the plantar surface and is locked in rigid equinus ‱ Anterior facet of the Calcaneus is absent and the Sustentaculum Tali is abnormal ‱ Lateral column is subluxed dorsolaterally at the Calcaneocuboid joint ‱ Cuboid and Navicular articulation with metatarsals and cuneiforms are normal
  • 12.
    Tendon and musclechanges ‱ All anterior muscle group tendons are contracted across the ankle joint ‱ Only the proximal section of the extensor retinaculum is present ‱ Extensors are displaced laterally ‱ Tibialis posterior tendon is attenuated as it passes inferior to the navicular ‱ Peroneal tendons are subluxed anterior to the malleoli ‱ Peroneal and Tibialis posterior tendons can act as dorsiflexors
  • 13.
    Ligamentous changes ‱ Tibionavicularband of the deltoid ligament is contracted ‱ Bifurcate, interosseous Talocalcaneal and Calcaneal fibular ligaments are shortened ‱ Distal band of the extensor retinaculum absent and the proximal part is thickened ‱ Ligaments along the medial plantar arch and long plantar ligament are attenuated ‱ Posterior ankle and subtalar joint capsules are contracted ‱ Plantar medial capsule of Talonavicular joint is elongated
  • 14.
    Vascular and nervechanges ‱ To date there are no physical complaints of vascular and nerve abnormalities ‱ Some abnormal histological exams have been reported ‱ Congenital Convex Pes Valgus can be associated with chronic proliferation endarteritis and neurofibromatosis
  • 15.
    Differential diagnosis ‱ TalipesCalcaneal Valgus - presents as flexible deformity ‱ Flexible vertical Talus ‱ Spastic flatfoot secondary to CP, and Myelmenigocele- can be reduced by using a nerve block to alleviate spasticity ‱ Flatfoot secondary to coalition
  • 16.
    Conservative treatment ‱ Objectis to restore the anatomic relationship of Calcaneus and Navicular to the Talus ‱ Conservative treatment alone is considered inadequate and surgery is the mainstay of treatment ‱ Casting alone gets poor results, but can be beneficial in stretching and manipulating anterior capsule and contracted muscles pre-operatively
  • 17.
    Surgical treatment ‱ Interventionis desired before 1 year of age ‱ Dodge proposed one stage open reduction and soft tissue release at ages less than 3 years old ‱ Grice arthrodesis is suggested for children ages 3 or greater ‱ Clark place bone block at the STJ at ages up to 3 years old, if greater than 3 years old perform STJ arthrodesis ‱ Griffen if surgery is delayed until 10-12 years old then perform triple arthrodesis ‱ Tachdijian ORIF if less than 4 years old and have failed casting and manipulation. If 4-6 years old, ORIF with TAL, posterior ankle and STJ capsule release, with STJ arthrodesis
  • 18.
    Tendon procedures ‱ TransferTibialis anterior tendon to Talar neck. Peroneus Brevis tendon is anastomosed with Tibialis posterior tendon and attached at the medial Navicular ‱ Duckworth and Smith Tibialis anterior tendon is transferred to the neck of the Talus ‱ Goldner comprehensive release 4 incision approach for release of all contracted joints and capsules, Tibialis anterior and posterior tendons are transferred to the neck of the Talus, Peroneus Brevis tendon is run through the neck of the Talus, Talonavicular joint and STJ are released
  • 20.
    Osseous procedures ‱ Talectomy(fallen out of favor) ‱ Removal of wedge from the Navicular under the Talar head to maintain elevation of the medial column ‱ Navicularectomy with release remains a very effective procedure ‱ Grice arthrodesis if less than 3 years of age ‱ Triple arthrodesis if 10-12 years of age
  • 22.
    McGlamry preference ‱ Startmanipulation and casting ASAP, twice a week for 6-8 weeks ‱ At 6-8 weeks attempt to relocate Talocalcanealnavicular joint and pin if successful ‱ If not reducible by 4-6 months correct deformity by ORIF ‱ Medial incision is made from 1st metatarsal/cuneiform joint to distal aspect of the medial malleolus and proximally to overlie Achilles tendon ‱ Lengthen the Achilles tendon
  • 23.
    McGlamry preference ‱ Lengthen:Tibialis anterior, and Peroneals ‱ Release: Talonavicular ligament, Tibionavicular ligament, Bifurcate ligament, Calcanealcuboid joint, Calcaneal Fibular liagament, Interosseous Talocalcaneal ligament ‱ Foot is distracted and manipulated and k-wire is placed from posterior Talar body through the Navicular and Cuneiform into IM space ‱ Reefing of the Spring ligament and placement of a 2nd k- wire from the plantar foot through the Calcaneus and into the Talus
  • 24.
    McGlamry preference ‱ Closeincision sites according to surgeon’s preference ‱ AK cast for 3-4 months ‱ Remove k-wire at 6 weeks ‱ Night time splint for 1 to 2 years ‱ Physical therapy ‱ Excise Navicular if the child is between the ages of 3-6 or the deformity remains ‱ Triple arthrodesis if the child is 10-12 years of age
  • 25.
    Post-op complications ‱ AVNof the Navicular or Talus ‱ Inadequate dorsiflexion ‱ Over correction of heel into Varus ‱ Development of bunion deformity ‱ Incomplete reduction ‱ Re-occurrence ‱ Continued Equinus ‱ Curly toes ‱ Stiffness
  • 26.