LEGG CALVE PERTHES
DISEASE
By Abdulrahman Sheha
Definition
Idiopathic avascular necrosis of
the proximal femoral epiphysis
in children.
Epidemiology
• ages 4-8 years
• 1 in 10,000 children
• Boys:Girls= 5:1
• Usually unilateral
• Higher among lower socioeconomic class
Etiology
• IDIOPATHIC
a. Disruption of the vascularity of the capital femoral
epiphysis.
b. Hydrostatic pressure theory.
Reactive synovitis > capsular distension > compression on retinacular
vessels
c. passive smoking (affects fibrinolysis)
Risk factors
• Short stature with delayed bone age (usually by two years).
(90%)
• Parents of the effected children are often elderly
• Low birth weight babies
• Associated congenital anomalies
• Protein C & S def.
Presentation
• Age 4-9 years.
• Intermittent pain in hip and a limp
• insidious onset
• Nature of pain : Aggravated by movement reileved by rest
• limp and pain in the groin, hip, commonly thigh, or knee
(referred pain).
Physical exam.
• Abnormal gait (antalgic).
• Decreased abduction and internal rotation.
• Late Limb-length inequality, is mild due to femoral head
collapse.
• Trendelenberg positive
Diagnostic tests
• X Ray (Best)
• Standard AP and frog-leg lateral views of the pelvis
• according to the stage
Radiographic stages (Waldenstrom)
a-Necrosis. (Ischemia stage). 6 months
b-Fragmentation (Revascularization) 6 months
c-Re ossification (healing) 18 month
d-Final (Remodeling) 3 years
Age at diagnosis is the most important prognostic factor
a-Early stage (Ischemia stage)
• Widening of the joint space and minor subluxation
• Irregular physeal plate
b-Fragmentation (Revascularization)
• Fragmentation and focal resorption of the
epiphysis.
• subchondral # (Crescent sign)
c-Reossification (healing)
• Normal bone density returns
• Alterations in shape of femoral head and neck
evident
d-Final (Remodeling)
• Changes depend on the severity the femoral head
• Coxa magna
Late Stage
• Coxa Magna.
• High-riding trochanter.
• Flattened femoral head.
• Irregular articular surface.
Classification
The Herring (lateral pillar) classification (most accurate)
• height of the lateral pillar of the capital epiphysis
on the AP view
Group A: Normal height
Group B: >50% maintained.
Group C: <50% maintained.
Cont. (Herring)
Treatment
Most patients (60%) with LCPD will NOT require surgical treatment.
Conservative (mainstay of management).
NSAIDs, painkillers, physiotherapy.
In patients with:
• Herring group A disease in any age group.
• Young age (< 6 years) at the onset of disease.
Cont.
Patients with poor prognosis will usually need containment
• >6 years old at the onset of the disease
• Female: mature earlier with less remodeling potential
• Obesity
• Progressive loss of hip motion
• Advanced stage of disease at diagnosis (B, C)
• Advanced grade (loss of containment).
Complications of Perthes disease.
a. Femoral head deformity.
* Premature physeal arrest patterns * Osteochondritis dissecans,
* Labral injury, and * Late osteoarthritis.
b. The most important prognostic factor
1- Shape of the femoral head and its congruency at skeletal maturity
2- patient age at onset of disease.
c. Degenerative changes in the hip joint in the fifth or sixth decade of life.

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  • 1.
  • 2.
    Definition Idiopathic avascular necrosisof the proximal femoral epiphysis in children.
  • 3.
    Epidemiology • ages 4-8years • 1 in 10,000 children • Boys:Girls= 5:1 • Usually unilateral • Higher among lower socioeconomic class
  • 4.
    Etiology • IDIOPATHIC a. Disruptionof the vascularity of the capital femoral epiphysis. b. Hydrostatic pressure theory. Reactive synovitis > capsular distension > compression on retinacular vessels c. passive smoking (affects fibrinolysis)
  • 5.
    Risk factors • Shortstature with delayed bone age (usually by two years). (90%) • Parents of the effected children are often elderly • Low birth weight babies • Associated congenital anomalies • Protein C & S def.
  • 6.
    Presentation • Age 4-9years. • Intermittent pain in hip and a limp • insidious onset • Nature of pain : Aggravated by movement reileved by rest • limp and pain in the groin, hip, commonly thigh, or knee (referred pain).
  • 7.
    Physical exam. • Abnormalgait (antalgic). • Decreased abduction and internal rotation. • Late Limb-length inequality, is mild due to femoral head collapse. • Trendelenberg positive
  • 8.
    Diagnostic tests • XRay (Best) • Standard AP and frog-leg lateral views of the pelvis • according to the stage
  • 9.
    Radiographic stages (Waldenstrom) a-Necrosis.(Ischemia stage). 6 months b-Fragmentation (Revascularization) 6 months c-Re ossification (healing) 18 month d-Final (Remodeling) 3 years Age at diagnosis is the most important prognostic factor
  • 10.
    a-Early stage (Ischemiastage) • Widening of the joint space and minor subluxation • Irregular physeal plate
  • 11.
    b-Fragmentation (Revascularization) • Fragmentationand focal resorption of the epiphysis. • subchondral # (Crescent sign)
  • 12.
    c-Reossification (healing) • Normalbone density returns • Alterations in shape of femoral head and neck evident
  • 13.
    d-Final (Remodeling) • Changesdepend on the severity the femoral head • Coxa magna
  • 14.
    Late Stage • CoxaMagna. • High-riding trochanter. • Flattened femoral head. • Irregular articular surface.
  • 15.
    Classification The Herring (lateralpillar) classification (most accurate) • height of the lateral pillar of the capital epiphysis on the AP view Group A: Normal height Group B: >50% maintained. Group C: <50% maintained.
  • 16.
  • 17.
    Treatment Most patients (60%)with LCPD will NOT require surgical treatment. Conservative (mainstay of management). NSAIDs, painkillers, physiotherapy. In patients with: • Herring group A disease in any age group. • Young age (< 6 years) at the onset of disease.
  • 18.
    Cont. Patients with poorprognosis will usually need containment • >6 years old at the onset of the disease • Female: mature earlier with less remodeling potential • Obesity • Progressive loss of hip motion • Advanced stage of disease at diagnosis (B, C) • Advanced grade (loss of containment).
  • 19.
    Complications of Perthesdisease. a. Femoral head deformity. * Premature physeal arrest patterns * Osteochondritis dissecans, * Labral injury, and * Late osteoarthritis. b. The most important prognostic factor 1- Shape of the femoral head and its congruency at skeletal maturity 2- patient age at onset of disease. c. Degenerative changes in the hip joint in the fifth or sixth decade of life.

Editor's Notes

  • #4 ضيف صورة الblood supply and eshrah 3leha 2el mechanim
  • #8 غيرها لصورة طفل